Mutations in MAGEL2 and L1CAM are associated with congenital hypopituitarism and arthrogryposis

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Congenital arthrogryposis associated with musculoskeletal defects in three newborn goats

Arthrogryposis as a congenital malformation that refers to the fixed flexion of one or more joints as a result of stiffness or limited movements of multiple joints, change of posture and limb function due to permanent contracture of joints and wasting of muscles that usually occur at early stage of gestation. This report describes congenital arthrogryposis associated with musculoskeletal defect...

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Arthrogryposis multiplex congenita (AMC) is characterized by the presence of multiple joint contractures resulting from reduced or absent fetal movement. Here, we report two unrelated families affected by lethal AMC. By genetic mapping and whole-exome sequencing in a multiplex family, a heterozygous truncating MAGEL2 mutation leading to frameshift and a premature stop codon (c.1996delC, p.Gln66...

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Evaluation of an Infant with Cholestasis and Congenital Hypopituitarism

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congenital arthrogryposis associated with musculoskeletal defects in three newborn goats

arthrogryposis as a congenital malformation that refers to the fixed flexion of one or more joints as a result of stiffness or limited movements of multiple joints, change of posture and limb function due to permanent contracture of joints and wasting of muscles that usually occur at early stage of gestation. this report describes congenital arthrogryposis associated with musculoskeletal defect...

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ژورنال

عنوان ژورنال: Yearbook of Paediatric Endocrinology

سال: 2020

ISSN: 1662-4009

DOI: 10.1530/ey.17.1.2